Objective: Exostosis of the internal auditory canal (IAC) is a rarely reported entity. We present a case of unilateral IAC exostosis with longitudinal radiographic imaging and its associated abnormal neurodiagnostic and audiologic studies. To our knowledge. this is the first documented report of a patient with hyperostosis of the IAC who was radiologically followed for over a decade. https://unitedssports.shop/product-category/fan-shop-oilers-jerseys/